ETFDH Antibody (PACO26561)
- SKU:
- PACO26561
- Product type:
- Antibody
- Reactivity:
- Pig
- Host Species:
- Rabbit
- Isotype:
- IgG
- Application:
- ELISA
- Antibody type:
- Polyclonal
- Conjugation:
- Unconjugated
Frequently bought together:
Description
| Antibody Name: | ETFDH Antibody (PACO26561) |
| Antibody SKU: | PACO26561 |
| Size: | 50ug |
| Host Species: | Rabbit |
| Tested Applications: | ELISA |
| Recommended Dilutions: | |
| Species Reactivity: | Pig |
| Immunogen: | Recombinant Pig Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial protein (34-617AA) |
| Form: | Liquid |
| Storage Buffer: | Preservative: 0.03% Proclin 300 Constituents: 50% Glycerol, 0.01M PBS, PH 7.4 |
| Purification Method: | >95%, Protein G purified |
| Clonality: | Polyclonal |
| Isotype: | IgG |
| Conjugate: | Non-conjugated |
| Background: | Accepts electrons from ETF and reduces ubiquinone. |
| Synonyms: | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial (ETF-QO) (ETF-ubiquinone oxidoreductase) (EC 1.5.5.1) (Electron-transferring-flavoprotein dehydrogenase) (ETF dehydrogenase), ETFDH |
| UniProt Protein Function: | ETFDH: Accepts electrons from ETF and reduces ubiquinone. Defects in ETFDH are the cause of glutaric aciduria type 2C (GA2C). GA2C is an autosomal recessively inherited disorder of fatty acid, amino acid, and choline metabolism. It is characterized by multiple acyl-CoA dehydrogenase deficiencies resulting in large excretion not only of glutaric acid, but also of lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Belongs to the ETF-QO/FixC family.Protein type: EC 1.5.5.1; Membrane protein, integral; Mitochondrial; Oxidoreductase |
| UniProt Protein Details: | |
| NCBI Summary: | |
| UniProt Code: | P55931 |
| NCBI GenInfo Identifier: | 298286807 |
| NCBI Gene ID: | 100515785 |
| NCBI Accession: | P55931.2 |
| UniProt Secondary Accession: | P55931 |
| UniProt Related Accession: | P55931, AAB30031 |
| Molecular Weight: | 80.8kD |
| NCBI Full Name: | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial |
| NCBI Synonym Full Names: | |
| NCBI Official Symbol: | ETFDH |
| NCBI Official Synonym Symbols: | ETF-QO |
| NCBI Protein Information: | electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial |
| UniProt Protein Name: | Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial |
| UniProt Synonym Protein Names: | Electron-transferring-flavoprotein dehydrogenase; ETF dehydrogenase |
| Protein Family: | Electron transfer flavoprotein-ubiquinone oxidoreductase |
| UniProt Gene Name: | ETFDH |
| UniProt Entry Name: |
Related Products
Human Electron Transferring Flavoprotein Dehydrogenase (ETFDH) ELISA Kit
Human Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial (ETFDH) ELISA Kit
Porcine Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial (ETFDH) ELISA Kit
